Neonatal Hemophagocytic Lymphohistiocytosis - Case Report (CROSBI ID 561564)
Prilog sa skupa u zborniku | sažetak izlaganja sa skupa | međunarodna recenzija
Podaci o odgovornosti
Roganović, Jelena ; Kvenić, Barbara ; Jonjić, Nives ; Seili-Bekafigo Irena ; Kardum-Skelin, Ika
engleski
Neonatal Hemophagocytic Lymphohistiocytosis - Case Report
Hemophagocytic lymphohystiocytosis (HLH) represents a severe hyperinflammatory condition with the cardinal symptoms prolonged fever, hepatosplenomegaly, and cytopenias. The most prominent histopathological feature is an accumulation of activated T lymphocytes and macrophages predominantly in lymphoid tissues. Although it can occur in all age groups, neonatal-onset HLH is very rare. We report on a case of HLH presenting with anemia and respiratory distress at birth. Several weeks prior to diagnosis the symptoms were attributed to a systemic infection. The child developed typical clinical and laboratory findings, and was diagnosed with HLH according to the HLH-2004 guidelines. Chemo-immunotherapy was initiated, but after a temporary control of the disease he succumbed to rapidly progressive HLH. Post-mortem, extensive hemophagocytosis was found in multiple organs. No specific genetic defect was identified. HLH is potentially fatal childhood disease. It is important for pediatricians to be able to early identify
Hemophagocytic lymphohystiocytosis
nije evidentirano
nije evidentirano
nije evidentirano
nije evidentirano
nije evidentirano
nije evidentirano
Podaci o prilogu
2009.
objavljeno
Podaci o matičnoj publikaciji
Knjiga sažetaka 4. Hrvatski kongres kliničke citologije, 1. Hrvatski simpozij analitičke citologije i 2. Hrvatski simpozij citotehnologije s međunarodnim sudjelovanjem
Kardum-Skelin, Ika ; Batinić, Drago ; Anić, Veronika
Zagreb: Hrvatsko društvo za kliničku citologiju ; Hrvatska udruga citotehnologa
Podaci o skupu
4. Hrvatski kongres kliničke citologije, 1. Hrvatski simpozij analitičke citologije i 2. Hrvatski simpozij citotehnologije s međunarodnim sudjelovanjem
poster
11.10.2009-14.10.2009
Split, Hrvatska