engleski

A case of retroperitoneal extra-gastrointestinal stromal tumor(E GIST)

Introduction: Primary neoplasms of the retroperitoneum are rare and maypose difficulty for the preoperative ethiologic diagnosis. Only a few cases of extragastrointestinal stromal tumor involving mesentery, retroperitoneum and the bladder have been reported. We report a patient with EGIST of the retroperitoneum. Case report: A6 years old man was hospitalised for evaluation of palpable mass in the abdomen. He had history of dyspeptic symptoms standard byochemistry was normal. Diagnostic work up disclosed a large septated cystic mass in retroperitoneal space. Intraoperative evaluation disclosed a well definded mass of 22cm in diameter not adhering to the surrounding tissues and unable a complete resection. Histology and immunohistochemistry disclosed relatively uniform large round sized cells positive for CD 34, vimentin, NSE, CGA and negative for S-100, actin, citokeratin and EMA. These findings were compatible with EGIST. Conclusion: EGIST represents a rare neoplasms, usually appearing as circumscribed masses, but our case presented as a huge cystic mass with solid portion. The diagnosis is confirm with histology and immunohistochemistryof the resected specimen. The reported patient is with large sized EGIST and low mitotic rate, that is significant for clinical outcome of EGIST. After the surgical resection the patient remaind well, during the follow up period of 2 years, without any additional specific drug treatment.

EGIST

nije evidentirano